Find best premium and Free Joomla templates at GetJoomlaTemplatesFree.com

Herlyn-Werner-Wunderlich Syndrome: A Case Report with Review of Literature - Abstract

Parag J Karkera, Pradnya Bendre, Mukunda Ramchandra, Flavia D’souza 

 

ABSTRACT

Herlyn-Werner-Wunderlich syndrome, a rare congenital anomaly of the urogenital tract involving Müllerian ducts and Wolffian structures, is characterized by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. It generally presents at puberty with pelvic pain, dysmenorrhea, and a vaginal or pelvic mass. The treatment consists of vaginal septectomy and marsupialization of the blind hemivagina to maintain patency. Long-term outcome is quite good with expectation of normal fertility in most cases. Herein we report a case of a 13 year old female child with Herlyn-Werner-Wunderlich syndrome with hematometra and hematocolpos and also discuss review of literature.

Keywords: Herlyn-Werner-Wunderlich syndrome, uterus didelphys, obstructed hemivagina, renal agenesis

 

Full Text (HTML) | PDF